Mullins’ syndrome: a new gammopathy-related autoinflammatory syndrome resistant to anakinra
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منابع مشابه
Mullins’ syndrome: a new gammopathy-related autoinflammatory syndrome resistant to anakinra
A 59-year-old Caucasian male had a 28-year history of episodes of recurrent urticaria, fever, periorbital angio-oedema and conjunctival injection. The episodes would be preceded by prodromal symptoms of nightmares, general malaise/fatigue and anterior chest/upper abdominal pain similar to indigestion. This would then proceed to urticaria, which had been described as atypical, not always being r...
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Schnitzler syndrome is a rare acquired systemic disease with a chronic evolution and difficult treatment. We report a 50-year-old woman with Schnitzler syndrome for 10 years, with major impact on her quality of life and refractory to conventional therapies. The patient was started on anakinra, an IL-1 receptor antagonist, with a rapid and sustained remission of the syndrome manifestations.
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Chronic urticaria may often be associated with interleukin (IL)-1-mediated autoinflammatory disease, which should be suspected if systemic inflammation signs are present. Here, we report a case of Schnitzler's syndrome without monoclonal gammopathy treated successfully with the IL-1 receptor antagonist anakinra. A 69-year-old man suffered from a pruritic urticarial rash for 12 years. It became ...
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The current massive vaccination brings a Janusfaced problem. There is a need to assess a positive effect but also to anticipate the abnormal immune response. Repeated administration of aluminum containing vaccines represents a possible risk factor for different aberrant reactions including the autoinflammatory syndrome that at this stage can be called enigmatic postvaccination phenomena. Descri...
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ژورنال
عنوان ژورنال: QJM
سال: 2012
ISSN: 1460-2725,1460-2393
DOI: 10.1093/qjmed/hcs208